Understanding left ventricular hypertrabeculation/noncompaction: pathomorphologic findings and prognostic impact of neuromuscular comorbidities

C Stöllberger, J Finsterer - Expert Review of Cardiovascular …, 2019 - Taylor & Francis
… mitochondrial disorders, Barth syndrome, zaspopathy, and myotonic dystrophy type 1. LVHT
does not seem to be a special type of cardiac involvement of NMDs. NMDs affect prognosis …

Left ventricular hypertrabeculation/noncompaction, cardiac phenotype, and neuromuscular disorders

C Stöllberger, C Wegner, J Finsterer - Herz, 2019 - search.proquest.com
… 2 9 Survival curves (death or cardiac transplantation) of 126 patients with the dilated phenotype
of left ventricular hypertrabeculation/ noncompaction depending on presence (light blue) …

[PDF][PDF] CTG-Repeat Size is Crucial for Assessing Cardiac Disease in Myotonic Dystrophy Type 1 by MRI

J Finsterer - Cardiol, 2019 - easpublisher.com
… J.,et al.,2014), and left ventricular hypertrabeculation (LVHT), … abnormalities in patients with
myotonic dystrophy type 1. Clin Res … , myotonic myopathy and hypotension traits of myotonic

Comprehensive investigations are required to manage cardiac disease in myotonic dystrophy 2

J Finsterer - Acta Neurologica Belgica, 2020 - Springer
… Though rarely occurring in MD2 [3], we should be informed how many of the included patients
presented with left ventricular hypertrabeculation (LVHT), also known as noncompaction …

Excessive Trabeculation of the Left Ventricle: JACC: Cardiovascular Imaging Expert Panel Paper

SE Petersen, B Jensen, N Aung, MG Friedrich… - Cardiovascular …, 2023 - jacc.org
… this fetus developed 1 week later. Forty-eight hours after delivery, left ventricular EF reduced
… same patient demonstrated progressive left ventricular dilatation with an left ventricular end-…

An overview of heart rhythm disorders and management in myotonic dystrophy type 1

TD Gossios, R Providencia, A Creta, OR Segal… - Heart Rhythm, 2022 - Elsevier
… Although left ventricular dysfunction was frequently detected in patients with VT, the only …
Additional structural abnormalities such as hypertrabeculation fulfilling noncompaction criteria …

[HTML][HTML] Outcome of Myotonic Dystrophy 1 Depends on Comprehensive Diagnostic and Therapeutic Management

J Finsterer, RN Ciudin, NC Dragatoiu, S Sipos… - Maedica, 2020 - ncbi.nlm.nih.gov
… develop systolic or diastolic dysfunction or left ventricular hypertrabeculation, also known as
… in myotonic dystrophy type 1 (Steinert disease) ... when there is an indication of ventricular

[PDF][PDF] Left ventricular trabeculation and noncompaction cardiomyopathy: a review

SI McFarlane - EC clinical and experimental anatomy, 2019 - researchgate.net
… like Myotonic dystrophies and Cobalamin … ventricular hypertrabeculation in the development
of LVNC. While gain of function mutations in certain genes and resulting hypertrabeculation

[HTML][HTML] The relationship between takotsubo syndrome, left ventricular hypertrabeculation/noncompaction, neurologic and neuromuscular disorders

C Stöllberger, J Finsterer - Reviews in Cardiovascular Medicine, 2021 - imrpress.com
… Most frequently associated with LVHT are mitochondrial disorders, Barth syndrome, zaspopathy,
myotonic dystrophy type 1, dystrobrevinopathy and Emery-Dreifuss muscular dystrophy

[HTML][HTML] Left ventricular noncompaction− Risk stratification and genetic consideration−

F Ichida - Journal of Cardiology, 2020 - Elsevier
hyper trabeculation/noncompaction, which is indistinguishable from congenital noncompaction,
has been reported in highly trained athletes [50], patients with myotonic dystrophy [51], …